3R62A

Structure of complement regulator factor h mutant, t1184r.
Total Genus 24
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The genus trace: a function that shows values of genus (vertical axis) for subchains spanned between the first residue, and all other residues (shown on horizontal axis). The number of the latter residue and the genus of a given subchain are shown interactively.

Total Genus
24
sequence length
125
structure length
125
Chain Sequence
GKCGPPPPIDNGDITSFPLSVYAPASSVEYQCQNLYQLEGNKRITCRNGQWSEPPKCLHPCVISREIMENYNIALRWRAKQKLYSRTGESVEFVCKRGYRLSSRSHTLRTTCWDGKLEYPTCAKR
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The genus matrix. At position (x,y) a genus value for a subchain spanned between x’th and y’th residue is shown. Values of the genus are represented by color, according to the scale given on the right.

Structure visualization

After clicking on a point (x,y) in the genus matrix above, a subchain from x to y is shown in color.

publication title Crystallographic determination of the disease-associated T1184R variant of the complement Factor H.
rcsb
molecule keywords Complement factor H
molecule tags Immune system
source organism Homo sapiens
total genus 24
structure length 125
sequence length 125
chains with identical sequence B
ec nomenclature
pdb deposition date 2011-03-21

pfam database annotations

chain Pfam Accession Code Pfam Family Identifier Pfam Description
A PF00084 Sushi Sushi repeat (SCR repeat)
Image from the rcsb pdb (www.rcsb.org)
cath code
ClassArchitectureTopologyHomologyDomain
2.10.70.10 Mainly Beta Ribbon Complement Module; domain 1 Complement Module, domain 1 3r62A01
2.10.70.10 Mainly Beta Ribbon Complement Module; domain 1 Complement Module, domain 1 3r62A02
5HZPB 1NWVA 2XRBA 3O8EB 1VVDA 2W80A 2EHFA 1OJWA 1HFIA 1HCCA 1GHQB 4ONTD 1TPMA 2W81A 3ERBA 1H2QP 3OEDC 3ZRZA 1HFHA 1O9AA 1CKLA 1LY2A 2MCZA 2B5ID 2JRAA 4J38B 2WIIC 4B2SA 3CALA 3GOVA 2QY0A 4A5WB 2YBYA 4CSYA 1TPNA 2O39C 5HYUB 1SRZA 1E88A 3TVJA 2JGXA 4AYDA 1OK1A 2YRAA 3RJ3D 3ZD1A 1ELVA 2CG6A 2MCYA 2RKZA 4AYMA 2V8EA 3R62A 3EJHA 1UOTP 2XWJI 4AYIA 3OP8A 4LOSA 4AYEA 4FXGG 1E5GA 2RLQA 1PPQA 5I0QB 4PZ5A 2KMSA 3NFPI 4F4OC 4ZH1D 1QO6A 1E8BA 1MD7A 1SS2A 2CG7A 2G7IA 2ERJA 1OJYA 1H03P 2EC3A 2RL0A 1GKNA 3IU3I 1OK9A 3M7PA 1QUBA 1GPZA 3OXUD 3L89M 4JHSA 3T5OA 1U5MA 2RKYA 1VVCA 1G4GA 3GXEA 1H04P 4IGDA 4MUCA 3SW0X 4WJG2 2JGWA 2RLPA 3KXVA 2IZ3A 5FO8C 1G4FA 3KZJA 2IZ4A 1ZJKA 3INBC 1OK3A 1QGBA 2XQWC 2XRDA 2UWNA 1TPGA 1OK2A 1H2PP 4YNXA 1Z92B 5HYTB 1FBRA 4B2RA 3ZD2A 4C16A 4DJZA 5HYPA 5JPMG 1C1ZA 1GKGA 1OJVA 2XWBF 2CKUA 3IX0A 4KKDA 2KRIA 4LOTA 1MD8A 2LOJA 4K12A 1Q3XA 2BZMA 2A55A 3MQLA
chains in the Genus database with same CATH superfamily
5HZPB 1NWVA 2XRBA 3O8EB 1VVDA 5DN5A 2W80A 2EHFA 1OJWA 1HFIA 1HCCA 1GHQB 4ONTD 1TPMA 2W81A 3ERBA 4BWCA 1H2QP 3OEDC 3ZRZA 1HFHA 1O9AA 3NJAA 1CKLA 1LY2A 2MCZA 2B5ID 2JRAA 4J38B 2WIIC 4B2SA 3CALA 3GOVA 2QY0A 3FGRA 3ZLEA 4A5WB 2Y8SA 2YBYA 1TPNA 2O39C 4CSYA 5HYUB 1SRZA 1E88A 3TVJA 2JGXA 4YIZA 4AYDA 1OK1A 2YRAA 3RJ3D 3ZD1A 1ELVA 2CG6A 2MCYA 3CI0J 4PO7A 2RKZA 4AYMA 2V8EA 2Y8RA 3R62A 3EJHA 1UOTP 3WSYA 2XWJI 4AYIA 3OP8A 4LOSA 2Y8TA 4AYEA 4FXGG 3K3TA 1E5GA 2RLQA 1PPQA 5I0QB 4PZ5A 2KMSA 3NFPI 4F4OC 4ZH1D 1QO6A 1E8BA 1MD7A 1SS2A 2CG7A 2G7IA 2ERJA 3F6KA 3FGTA 1OJYA 1H03P 2EC3A 2RL0A 1GKNA 3IU3I 1OK9A 3M7PA 1QUBA 1GPZA 3OXUD 3L89M 4JHSA 3T5OA 4APLA 1U5MA 3WSXA 2RKYA 1VVCA 1G4GA 3GXEA 1H04P 4IGDA 4MUCA 3SW0X 4WJG2 2JGWA 2RLPA 3KXVA 2IZ3A 4N7EA 5FO8C 1G4FA 5DN4A 3KZJA 2IZ4A 1ZJKA 3INBC 1OK3A 1QGBA 2XQWC 3ZLDA 2XRDA 2UWNA 1TPGA 1OK2A 1H2PP 4YNXA 1Z92B 1RLHA 5HYTB 2X2ZA 1FBRA 4B2RA 3ZD2A 3VWOA 4C16A 4DJZA 5HYPA 5JPMG 1C1ZA 1GKGA 1OJVA 2ZYCA 2I2LA 2XWBF 2CKUA 3IX0A 4KKDA 2KRIA 4LOTA 4MSLA 1MD8A 2LOJA 4K12A 1Q3XA 2BZMA 2A55A 3MQLA
chains in the Genus database with same CATH topology
5HZPB 1NWVA 2XRBA 3O8EB 1VVDA 2W80A 2EHFA 1OJWA 1HFIA 1HCCA 1GHQB 4ONTD 1TPMA 2W81A 3ERBA 1H2QP 3OEDC 3ZRZA 1HFHA 1O9AA 1CKLA 1LY2A 2MCZA 2B5ID 2JRAA 4J38B 2WIIC 4B2SA 3CALA 3GOVA 2QY0A 4A5WB 2YBYA 4CSYA 1TPNA 2O39C 5HYUB 1SRZA 1E88A 3TVJA 2JGXA 4AYDA 1OK1A 2YRAA 3RJ3D 3ZD1A 1ELVA 2CG6A 2MCYA 2RKZA 4AYMA 2V8EA 3R62A 3EJHA 1UOTP 2XWJI 4AYIA 3OP8A 4LOSA 4AYEA 4FXGG 1E5GA 2RLQA 1PPQA 5I0QB 4PZ5A 2KMSA 3NFPI 4F4OC 4ZH1D 1QO6A 1E8BA 1MD7A 1SS2A 2CG7A 2G7IA 2ERJA 1OJYA 1H03P 2EC3A 2RL0A 1GKNA 3IU3I 1OK9A 3M7PA 1QUBA 1GPZA 3OXUD 3L89M 4JHSA 3T5OA 1U5MA 2RKYA 1VVCA 1G4GA 3GXEA 1H04P 4IGDA 4MUCA 3SW0X 4WJG2 2JGWA 2RLPA 3KXVA 2IZ3A 5FO8C 1G4FA 3KZJA 2IZ4A 1ZJKA 3INBC 1OK3A 1QGBA 2XQWC 2XRDA 2UWNA 1TPGA 1OK2A 1H2PP 4YNXA 1Z92B 5HYTB 1FBRA 4B2RA 3ZD2A 4C16A 4DJZA 5HYPA 5JPMG 1C1ZA 1GKGA 1OJVA 2XWBF 2CKUA 3IX0A 4KKDA 2KRIA 4LOTA 1MD8A 2LOJA 4K12A 1Q3XA 2BZMA 2A55A 3MQLA
chains in the Genus database with same CATH homology


 
#chains in the Genus database with same CATH superfamily
 5HZP B;  1NWV A;  2XRB A;  3O8E B;  1VVD A;  2W80 A;  2EHF A;  1OJW A;  1HFI A;  1HCC A;  1GHQ B;  4ONT D;  1TPM A;  2W81 A;  3ERB A;  1H2Q P;  3OED C;  3ZRZ A;  1HFH A;  1O9A A;  1CKL A;  1LY2 A;  2MCZ A;  2B5I D;  2JRA A;  4J38 B;  2WII C;  4B2S A;  3CAL A;  3GOV A;  2QY0 A;  4A5W B;  2YBY A;  4CSY A;  1TPN A;  2O39 C;  5HYU B;  1SRZ A;  1E88 A;  3TVJ A;  2JGX A;  4AYD A;  1OK1 A;  2YRA A;  3RJ3 D;  3ZD1 A;  1ELV A;  2CG6 A;  2MCY A;  2RKZ A;  4AYM A;  2V8E A;  3R62 A;  3EJH A;  1UOT P;  2XWJ I;  4AYI A;  3OP8 A;  4LOS A;  4AYE A;  4FXG G;  1E5G A;  2RLQ A;  1PPQ A;  5I0Q B;  4PZ5 A;  2KMS A;  3NFP I;  4F4O C;  4ZH1 D;  1QO6 A;  1E8B A;  1MD7 A;  1SS2 A;  2CG7 A;  2G7I A;  2ERJ A;  1OJY A;  1H03 P;  2EC3 A;  2RL0 A;  1GKN A;  3IU3 I;  1OK9 A;  3M7P A;  1QUB A;  1GPZ A;  3OXU D;  3L89 M;  4JHS A;  3T5O A;  1U5M A;  2RKY A;  1VVC A;  1G4G A;  3GXE A;  1H04 P;  4IGD A;  4MUC A;  3SW0 X;  4WJG 2;  2JGW A;  2RLP A;  3KXV A;  2IZ3 A;  5FO8 C;  1G4F A;  3KZJ A;  2IZ4 A;  1ZJK A;  3INB C;  1OK3 A;  1QGB A;  2XQW C;  2XRD A;  2UWN A;  1TPG A;  1OK2 A;  1H2P P;  4YNX A;  1Z92 B;  5HYT B;  1FBR A;  4B2R A;  3ZD2 A;  4C16 A;  4DJZ A;  5HYP A;  5JPM G;  1C1Z A;  1GKG A;  1OJV A;  2XWB F;  2CKU A;  3IX0 A;  4KKD A;  2KRI A;  4LOT A;  1MD8 A;  2LOJ A;  4K12 A;  1Q3X A;  2BZM A;  2A55 A;  3MQL A; 
#chains in the Genus database with same CATH topology
 5HZP B;  1NWV A;  2XRB A;  3O8E B;  1VVD A;  5DN5 A;  2W80 A;  2EHF A;  1OJW A;  1HFI A;  1HCC A;  1GHQ B;  4ONT D;  1TPM A;  2W81 A;  3ERB A;  4BWC A;  1H2Q P;  3OED C;  3ZRZ A;  1HFH A;  1O9A A;  3NJA A;  1CKL A;  1LY2 A;  2MCZ A;  2B5I D;  2JRA A;  4J38 B;  2WII C;  4B2S A;  3CAL A;  3GOV A;  2QY0 A;  3FGR A;  3ZLE A;  4A5W B;  2Y8S A;  2YBY A;  1TPN A;  2O39 C;  4CSY A;  5HYU B;  1SRZ A;  1E88 A;  3TVJ A;  2JGX A;  4YIZ A;  4AYD A;  1OK1 A;  2YRA A;  3RJ3 D;  3ZD1 A;  1ELV A;  2CG6 A;  2MCY A;  3CI0 J;  4PO7 A;  2RKZ A;  4AYM A;  2V8E A;  2Y8R A;  3R62 A;  3EJH A;  1UOT P;  3WSY A;  2XWJ I;  4AYI A;  3OP8 A;  4LOS A;  2Y8T A;  4AYE A;  4FXG G;  3K3T A;  1E5G A;  2RLQ A;  1PPQ A;  5I0Q B;  4PZ5 A;  2KMS A;  3NFP I;  4F4O C;  4ZH1 D;  1QO6 A;  1E8B A;  1MD7 A;  1SS2 A;  2CG7 A;  2G7I A;  2ERJ A;  3F6K A;  3FGT A;  1OJY A;  1H03 P;  2EC3 A;  2RL0 A;  1GKN A;  3IU3 I;  1OK9 A;  3M7P A;  1QUB A;  1GPZ A;  3OXU D;  3L89 M;  4JHS A;  3T5O A;  4APL A;  1U5M A;  3WSX A;  2RKY A;  1VVC A;  1G4G A;  3GXE A;  1H04 P;  4IGD A;  4MUC A;  3SW0 X;  4WJG 2;  2JGW A;  2RLP A;  3KXV A;  2IZ3 A;  4N7E A;  5FO8 C;  1G4F A;  5DN4 A;  3KZJ A;  2IZ4 A;  1ZJK A;  3INB C;  1OK3 A;  1QGB A;  2XQW C;  3ZLD A;  2XRD A;  2UWN A;  1TPG A;  1OK2 A;  1H2P P;  4YNX A;  1Z92 B;  1RLH A;  5HYT B;  2X2Z A;  1FBR A;  4B2R A;  3ZD2 A;  3VWO A;  4C16 A;  4DJZ A;  5HYP A;  5JPM G;  1C1Z A;  1GKG A;  1OJV A;  2ZYC A;  2I2L A;  2XWB F;  2CKU A;  3IX0 A;  4KKD A;  2KRI A;  4LOT A;  4MSL A;  1MD8 A;  2LOJ A;  4K12 A;  1Q3X A;  2BZM A;  2A55 A;  3MQL A; 
#chains in the Genus database with same CATH homology
 5HZP B;  1NWV A;  2XRB A;  3O8E B;  1VVD A;  2W80 A;  2EHF A;  1OJW A;  1HFI A;  1HCC A;  1GHQ B;  4ONT D;  1TPM A;  2W81 A;  3ERB A;  1H2Q P;  3OED C;  3ZRZ A;  1HFH A;  1O9A A;  1CKL A;  1LY2 A;  2MCZ A;  2B5I D;  2JRA A;  4J38 B;  2WII C;  4B2S A;  3CAL A;  3GOV A;  2QY0 A;  4A5W B;  2YBY A;  4CSY A;  1TPN A;  2O39 C;  5HYU B;  1SRZ A;  1E88 A;  3TVJ A;  2JGX A;  4AYD A;  1OK1 A;  2YRA A;  3RJ3 D;  3ZD1 A;  1ELV A;  2CG6 A;  2MCY A;  2RKZ A;  4AYM A;  2V8E A;  3R62 A;  3EJH A;  1UOT P;  2XWJ I;  4AYI A;  3OP8 A;  4LOS A;  4AYE A;  4FXG G;  1E5G A;  2RLQ A;  1PPQ A;  5I0Q B;  4PZ5 A;  2KMS A;  3NFP I;  4F4O C;  4ZH1 D;  1QO6 A;  1E8B A;  1MD7 A;  1SS2 A;  2CG7 A;  2G7I A;  2ERJ A;  1OJY A;  1H03 P;  2EC3 A;  2RL0 A;  1GKN A;  3IU3 I;  1OK9 A;  3M7P A;  1QUB A;  1GPZ A;  3OXU D;  3L89 M;  4JHS A;  3T5O A;  1U5M A;  2RKY A;  1VVC A;  1G4G A;  3GXE A;  1H04 P;  4IGD A;  4MUC A;  3SW0 X;  4WJG 2;  2JGW A;  2RLP A;  3KXV A;  2IZ3 A;  5FO8 C;  1G4F A;  3KZJ A;  2IZ4 A;  1ZJK A;  3INB C;  1OK3 A;  1QGB A;  2XQW C;  2XRD A;  2UWN A;  1TPG A;  1OK2 A;  1H2P P;  4YNX A;  1Z92 B;  5HYT B;  1FBR A;  4B2R A;  3ZD2 A;  4C16 A;  4DJZ A;  5HYP A;  5JPM G;  1C1Z A;  1GKG A;  1OJV A;  2XWB F;  2CKU A;  3IX0 A;  4KKD A;  2KRI A;  4LOT A;  1MD8 A;  2LOJ A;  4K12 A;  1Q3X A;  2BZM A;  2A55 A;  3MQL A; 
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similar chains in the Genus database (?% sequence similarity)
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similar chains in the pdb database (?% sequence similarity)

 
#similar chains in the Genus database (?% sequence similarity)
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#similar chains, but unknotted
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